Listen to pronunciation. (FY-broh-muh-TOH-sis) A condition in which multiple fibromas develop. Fibromas are tumors (usually benign) that affect connective tissue.

What is congenital myofibromatosis?

Infantile myofibromatosis is a rare disorder characterized by the growth of one or more noncancerous (benign) tumors affecting the skin, bone, muscle, soft tissue, and rarely the internal organs (viscera).

How common is Myofibroma?

How common is infantile myofibromatosis? IM is found at birth in about 1 out of 150,000 babies. Some cases of IM may not be diagnosed or correctly diagnosed.

What are the symptoms of fibromatosis?

A fibroma is a benign, tumor-like growth made up mostly of fibrous or connective tissue. … Common symptoms of a plantar fibroma

How is fibromatosis treated?

Treatment options include surgery, nonsteroidal anti-inflammatory drugs with or without hormonal manipulation, chemotherapy, radiation therapy, and other forms of local therapy. Many treatments have been used, but these are not without toxicities.

What is infantile fibrosarcoma?

Infantile or congenital fibrosarcoma: This type of tumor is the most common soft tissue sarcoma found in children under one year of age. It presents as a rapidly growing mass at birth or shortly after. This fibrosarcoma is usually slow-growing.

What is nodular fasciitis?

Nodular fasciitis is a fast-growing lump in your soft tissue. It’s not clear why you get it, but it’s not cancerous. It’s sometimes called pseudosarcomatous fasciitis, proliferative fasciitis, or infiltrative fasciitis. It’s a noncancerous skin growth in your soft tissue.

Is Myofibroma benign?

Myofibroma is a benign fibrous tumour. It is most commonly a solitary lesion arising in the first 2 years of life, when it is also called solitary infantile myofibroma. It is thought to be of myofibroblastic origin.

Who is Myofibroma?

Myofibroma (unifocal) and myofibromatosis (multifocal) are rare spindle cell neoplasms composed of myofibroblasts, i.e., cells with characteristics intermediate between smooth muscle, fibroblasts, and undifferentiated cells. These lesions typically appear in children and infants.

What is Myofibroblastoma?

Myofibroblastoma of the breast is an uncommon benign stromal tumor, predominantly occurring in menopausal women and older men. The clinical presentation is characterized by a mobile, well defined and solid palpable tumor.

Is fibromatosis serious?

Head and neck desmoid fibromatosis is a serious condition due to local aggression, specific anatomical patterns and the high rate of relapse. For children surgery is particularly difficult, given the potential for growth disorders. Treatment includes prompt radical excision with a wide margin and/or radiation.

Is fibromatosis curable?

Abstract — Fibromatosis or desmoid tumors are locally aggressive neoplasms that have a propensity for local invasion and recurrence. The mainstay of treatment is excision with negative margins and the role of radiotherapy is controversial.

Can fibromatosis be cancerous?

Desmoid tumor is called aggressive fibromatosis as it has similarities with a malignant (cancerous) tumor called fibrosarcoma. However, it is considered benign because it does not metastasize (spread) to other parts of the body.

What is the cause of fibromatosis?

What causes fibromatosis? The cause of fibromatosis remains unclear. In some types of fibromatosis such as desmoid tumours, it is thought that the condition may be related to trauma, hormonal factors, or have a genetic association.

Is a fibromatosis a tumor?

Deep or aggressive fibromatosis, also known as desmoid-type fibromatosis (DTF) or desmoid tumor, is a clonal locally invasive tumor that does not metastasize.

Is fibromatosis contagious?

The manner in which the disease is transmitted is not entirely known. However, it has been suggested that transmission occurs through direct contact between broken skin and infectious material, either from a fibroma of an another infected deer or vegetation that has come in contact with an infected deer.

How common is infantile fibrosarcoma?

Infantile fibrosarcoma represents less than 1% of all childhood cancers, but it is the most common soft-tissue sarcoma in those under 1 year of age.

Do Histiocytomas go away?

Histiocytomas are considered highly treatable skin masses. Though they will typically regress spontaneously within a couple of months, they don’t always do so quickly or completely enough for a veterinarian’s (or owner’s) comfort.

Can fibrosarcoma be cured?

Treatment for fibrosarcoma remains focused on treatment of the primary tumor. Surgery is the only curative treatment for these tumors available, and radiation is often used when the tumor measures at least 5 cm (2 inches) in size.

Is nodular fasciitis painful?

Nodular fasciitis is a benign fibroblastic lesion that was historically misdiagnosed as a malignant neoplasm. Patients present with pain and swelling of relatively brief duration. The clinical presentation is suggestive of an aggressive lesion, usually occurring in muscle fascia.

What are soft nodules?

Soft tissue tumors are cell growths that emerge nearly anywhere in the body: in tendons, muscles, ligaments, cartilage, nerves, blood vessels, fat, and other tissues. Patients commonly refer to these masses as lumps or bumps.

Where are nodules found?

Nodules can develop just below the skin. They can also develop in deeper skin tissues or internal organs. Dermatologists use nodules as a general term to describe any lump underneath the skin that’s at least 1 centimeter in size.

What is Myopericytoma?

Listen to pronunciation. (my-oh-PAYR-ih-sy-TOH-muh) A rare, slow-growing soft tissue tumor that begins in cells that wrap around blood vessels. Most myopericytomas are benign (not cancer).

What is Fibrosis sarcoma?

Fibrosarcoma is a malignant neoplasm (cancer) of mesenchymal cell origin in which histologically the predominant cells are fibroblasts that divide excessively without cellular control; they can invade local tissues and travel to distant body sites (metastasize).